• Developmental Dysplasia of the Hip is a disorder of abnormal development of the hip secondary to capsular laxity and mechanical instability.
  • DDH encompasses a spectrum of disease that includes
    • dysplasia
      • shallow or underdeveloped acetabulum
    • subluxation
      • displacement of the joint with some contact remaining between the articular surfaces
    • dislocation
      • complete displacement of the joint with no contact between the original articular surfaces
  • Epidemiology
    • Incidence
      • most common hip orthopaedic disorder in newborns
      • dysplasia is 1:100
      • dislocation is 1:1000
    • Demographics
      • more common infemales (6:1)
    • Anatomic location
      • most common inleft hip (60%)
        • due to the most common intrauterine position being left occiput anterior (left hip is adducted against the mother’s lumbrosacral spine)
      • bilateral in 20%
    • Risk factors
      • firstborn
        • due to unstretched uterus and tight abdominal structures compressing the uterus
      • female
        • due to increased ligamentous laxity that transiently exists as the result of circulating maternal hormones and the estrogens produced by the fetal uterus
      • breech
        • more commonly seen in female children, firstborn children, and pregnancies complicated by oligohydramnios
        • higher risk of DDH with frank/single breech position compared to footling breech position
      • family history
      • oligohydramnios
      • macrosomia
      • limited hip abduction
      • talipes
      • swaddling
    • Pathophysiology
      • etiology
        • initial instability thought to be caused by maternal and fetal laxity, genetic laxity, and intrauterine and postnatal malpositioning
      • pathoanatomy
        • initial instability leads to dysplasia
          • typical deficiency is anterior or anterolateral acetabulum
            • in spastic cerebral palsy, acetabular deficiency is posterosuperior 
          • dysplasia leads to subluxation and gradual dislocation
            • repetitive subluixation of the femoral head leads to the formation of a ridge of thickened articular cartilage called thelimbus
          • chronic dislocation leads to
            • development of secondary barriers to reduction
              • pulvinar thickens
              • ligamentum teres thickens and elongates
              • transverse acetabular ligament hypertrophies
              • hip capsule and iliopsoas form hourgass configuration
            • anatomic changes
              • increased femoral anteversion
              • flattening of the femoral head
              • increased acetabular anteversion
              • increased obliquity and decreased concavity of the acetabular roof
              • thickening of the medial acetabular wall
            • Associated conditions
              • congenital muscular torticollis(20%)
              • metatarsus adductus(10%)
              • congenital knee dislocation
            • conditions characterized by increased amounts of type III collagen
          • Presentation
            • Physical exam (< 3 months)
              • mainstay of physical diagnosis is palpable hip subluxation/dislocation on exam 
                • Barlow
                  • dislocates adislocatable hip by adduction and depression of the flexed femur
                  • “click of exit”
                • Ortolani   
                  • reduces adislocated hip by elevation and abduction of the flexed femur
                  • “click of entry”
                • Galeazzi (Allis)
                  • apparent limb length discrepancy due to aunilateral dislocated hip with hip flexed at 90 degrees and feet on the table
                  • femur appears shortened on dislocated side
                • Barlow and Ortolani are rarely positive after 3 months of age because of soft-tissue contractures that form around the hip
              • Physical exam (> 3 months to 1 year)
                • limitations in hip abduction  
                  • most sensitive test once contractures have begun to occur
                  • occurs as laxity resolves and stiffness begins to occur
                  • decreased symmetrically in bilateral dislocations
                • leg length discrepancy predominates
                • Klisic test
                  • used to detect bilateral dislocations
                  • line from the long finger placed over the greater trochanter and the index finger over the ASIS should point to the umbilicus
                  • if the hip is dislocated, the line will point halfway between the umbilicus and pubis
                • Physical exam (> 1 year – walking child)
                  • pelvic obliquity
                  • lumbar lordosis
                    • in response to hip contractures resulting from bilateral dislocations in a child of walking age
                  • Trendelenburg gait
                    • results from abductor insufficiency
                  • toe-walking
                    • attempt to compensate for the relative shortening of the affected side
                  • Imaging
                    • Radiograph
                      • indications
                        • becomes primary imaging modality at 4-6 moafter the femoral head begins to ossify  
                        • positive physical exam
                        • leg length discrepancy
                      • recommended views
                        • AP of pelvis
                      • measurements
                        • hip dislocation
                          • Hilgenreiner’s line
                            • horizontal line through the right and left triradiate cartilage
                            • femoral head ossification should beinferior to this line
                          • Perkin’s line 
                            • line perpendicular to Hilgenreiner’s line through a point at the lateral margin of the acetabulum
                            • femoral head ossification should bemedial to this line
                          • Shenton’s line 
                            • arc along the inferior border of the femoral neck and the superior margin of the obturator foramen
                            • arc line should becontinuous
                          • delayed ossification of the femoral head is seen in cases of dislocation
                          • acetabular teardrop not typically present prior to hip reduction for chronic dislocations since birth  
                            • development of teardrop after reduction is thought to be a good prognostic sign for hip function
                          • hip dysplasia
                            • acetabular index (AI)
                              • angle formed by Hilgenreiner’s line and a line from a point on the lateral triradiate cartilage to a point on lateral margin of acetabulum
                              • should be < 25° in patients older than 6 months 
                            • center-edge angle (CEA) of Wiberg
                              • angle formed by Perkin’s line and a line from the center of the femoral head to the lateral edge of the acetabulum
                              • < 20° is considered abnormal
                              • only reliable in patients > 5 years old
                            • Ultrasound
                              • indications
                                • primary imaging modality from birth to 4 months
                                  • may produce spurious results if performed before 4-6 weeks of age
                                • positive physical exam
                                • risk factors (family history or breech presentation)
                                  • AAP recommends an US study at 6 weeks in patients who are considered high risk (family history or breech presentation) despite normal exam
                                • monitoring of reductionduring Pavlik harness treatment   
                                • most studies show it is not cost effective for routine screening
                              • findings
                                • evaluates for acetabular dysplasia and/or the presence of a hip dislocation
                                • allows view of bony acetabular anatomy, femoral head, labrum, ligamentum teres, hip capsule  
                                • normal ultrasound in patients with soft-tissue clicks will have normal acetabular development
                              • measurements
                                • alpha angle  
                                  • angle created by lines along the bony acetabulum and the ilium
                                  • normal is > 60°
                                • beta angle
                                  • angle created by lines along the labrum and the ilium
                                  • normal is < 55°
                                • femoral head is normally bisected by a line drawn down from the ilium
                              • staging
                                • Graf classification
                              • Screening
                                • All infants require screening
                                  • physical exam
                                    • successful screening requires repetitive screening until walking age
                                  • ultrasound
                                    • ultrasound screening of all infants occurs in many countries; however, it has not been proven to be cost-effective
                                    • recommendation is to perform ultrasound at 4-6 weeks in patients with
                                      • risk factors
                                      • positive physical findings
                                    • Treatment in children
                                      • Non-operative
                                        • Pavlik harness     
                                          • indications
                                            • < 6 months old andreducible hip
                                          • contraindicated in teratologic hip dislocations and patients with spina bifida or spasticity
                                            • requires normal muscle function for successful outcomes
                                          • closed reduction and spica casting
                                            • indications
                                              • 6-18 months old
                                              • failure of Pavlik treatment
                                            • Operative
                                              • open reduction and spica casting    
                                                • indications
                                                  • > 18 months old
                                                  • failure of closed reduction
                                                • open reduction and femoral osteotomy  
                                                  • indications
                                                    • > 2 years old with residual hip dysplasia
                                                    • anatomic changes on femoral side (e.g., femoral anteversion, coxa valga)
                                                    • best in younger children (< 4 years old)
                                                      • after 4 years old, pelvic osteotomies are utilized
                                                    • open reduction and pelvic osteotomy
                                                      • indications
                                                        • > 2 years old with residual hip dysplasia
                                                        • severe dysplasia accompanied by significant radiographic changes on the acetabular side (increased acetabular index)   
                                                        • used more commonly in older children (> 4 yr)
                                                          • decreased potential for acetabular remodeling as child ages
                                                        • Complications
                                                          • AVN
                                                            • seen with all forms of treatment
                                                            • increased rates associated with
                                                              • excessive orforceful abduction
                                                              • previousfailed closed treatment
                                                              • repeat surgery
                                                            • diagnosis based on radiographic findings that include
                                                              • failure of appearance or growth of the ossific nucleus 1 year after the reduction
                                                              • broadening of the femoral neck
                                                              • increased density and fragmentation of ossified femoral head
                                                              • residual deformity of proximal femur after ossification
                                                            • Delayed diagnosis
                                                              • bilateral dislocations
                                                                • patients typically function better if hips are not reduced if 6 years of age or older
                                                              • unilateral dislocation
                                                                • better outcomes without surgical treatment if the patient is > 8 years old
                                                                • epiphysiodesis can be performed for treatment of limb length discrepancy
                                                              • Recurrence
                                                                • approximately 10% with appropriate treatment
                                                                • requires radiographic follow-up until skeletal maturity